Ibiglustat|Genz-682452|SAR402671

Ibiglustat|Genz-682452|SAR402671

DC Chemicals, Website: www.dcchemicals.com

Product Name: Ibiglustat(Genz-682452）|Cas Number: 1401090-53-6| Catalog Number: DC10007|Other Nmaes: GZ-402671; GZ402671; GZ402671; SAR402671; SAR-402671; SAR 402671; Genz-682452-AA; Ibiglustat; GZ-452; Genz-682452

Ibiglustat (Genz-682452,SAR402671), is a potent and selective Glucosylceramide synthase inhibitor and ceramide glucosyltransferase inhibitor.

Ibiglustat, also known as GZ402671, GZ-452; Genz-682452 and SAR402671, is a potent and selective Glucosylceramide synthase inhibitor and ceramide glucosyltransferase inhibitor. Ibiglustat blocks the formation of glucosylceramide (GL-1), a key intermediate in the synthesis of GL-3. Ibiglustat is potentially useful for treating Fabry disease. Fabry disease is a rare lysosomal storage disorder, which results in abnormal tissue deposits of a particular fatty substance called globotriaosylceramide (GL-3 or Gb3) throughout the body.